目的:总结54例Chiari畸形合并脊髓空洞症的显微外科手术治疗经验。方法:本组对1998年9月至2005年9月共收治的54例Chiari畸形合并脊髓空洞症患者采用后路手术入路,对颅底凹陷症采用后路减压,显微镜下行小脑扁桃体软膜下部分切除,正中孔开放手术治疗。结果:54例患者术中观察发现延髓和上颈髓明显受压和不同程度同小脑扁桃体粘连,正中孔引流不畅;随访1月~7年,术后42例症状显著改善,12例明显改善;影像学复查提示脊髓空洞明显缩小。结论:显微外科手术治疗Chiari畸形合并脊髓空洞症疗效确切可靠。
Citation:
LIU Yunshi,WU Ke,LI Dekang,et al. Microsurgical Treatment for ArnoldChiari Malformation with Syringomyelia. West China Medical Journal, 2009, 24(2): 315-316. doi:
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- 1. Badie B,Mendoza D,Batzdorf U.Posterior fpssa volume and response to suboccipital decompression in patients with Chiari Ⅰmalformation[J].Neurosurgery,1995,37:214-218..
- 2. 章翔,易声禹,吴声伶,等.ArnoldChiari畸形的诊断与治疗[J].中华神经外科杂志,1992,8:2930..
- 3. 马稚如,戴以武,郑文济,等.ArnoldChiari畸形的诊断和外科治疗[J].中华神经外科杂志,1996,12:308-309..
- 4. 栗世方,周茂德,雷学,等.ChiariⅠ畸形合并脊髓空洞症的发病机制及外科治疗探讨[J].临床神经外科医学,2003,5(4):165-167..
- 5. 刘勇,潘昕,倪鸣山,等.Chiari畸形合并脊髓空洞症的临床分类和手术方式探讨[J].中国临床神经外科杂志[J],2003,8(6):446-447..
- 6. 朱士广,杨树源.中央部分椎板切除行脊髓空洞腹腔分流手术[J].中华神经外科杂志,2005,21(6):350-351..
- 7. 黄思庆,肖启华,李国平,等.ArnoldChiari畸形合并脊髓空洞症的显微外科治疗310例临床分析[J].中华神经外科杂志,2005,21(2):100-102..
- 8. Tator CH,Meguro K,Rowed DW.Favorable results with syringosubarachnoid shunt for treatment of syringomyelia[J].J Neurosurgery,1982,56(4):517-523..
- 9. Brugieres P,IdyPeretti I,Iffenecker C,et al.CSF flow measurement in syringomyelia[J].AJNR Am J Neuroradiol,2000,21:1785-1792..
- 10. Gardner WJ,Hydrodynamic mechanism of syringomyelia[J].J Neurol Neurosurg Psychiatry,1965,28:274-259..
- 11. Hoffman HJ,Neill J,Crone KR,et al.Hydrosyringomyelia and its management in childhood[J].Neurosurgery,1987,21(3):347-351..
- 12. Williams B.Pathogenesis of syringomyelia[J].Lancet,1972,2(7784):969-970..
- 13. Williams B.Progress in syringomyelia[J].Neurol Res,1986,8(3):130-145..